基因编辑仓鼠F508del CFTR with two altered RXR motifs escapes from ER quality control but its channel activity is thermally sensitive.
期刊:Biochimica et biophysica acta发表年份:2006作者:Tamás Hegedus; Andrei Aleksandrov; Liying Cui; Martina Gentzsch; Xiu-Bao Chang; John R Riordan
